D47.01

Billable

Cutaneous mastocytosis

Neoplasms (C00-D49)

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Also Known As

Diffuse cutaneous mastocytosisMaculopapular cutaneous mastocytosisSolitary mastocytomaTelangiectasia macularis eruptiva perstansUrticaria pigmentosa

Excludes1

direct

Cannot be coded with D47.01

  • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
  • congenital urticaria pigmentosa (Q82.2)
  • extracutaneous mastocytoma (D47.09)

Excludes1

inherited from D47.0

Rules from parent category D47.0: Mast cell neoplasms of uncertain behavior

  • congenital cutaneous mastocytosis (Q82.2)
  • histiocytic neoplasms of uncertain behavior (D47.Z9)
  • malignant mast cell neoplasm (C96.2-)

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Code Information

CodeD47.01
BillableYes
ParentD47.0
CategoryNeoplasms (C00-D49)
Excludes16 rule(s)
Excludes20 note(s)

Data Source

CMS ICD-10-CM 2026 Tabular List

Updated October 1, 2025 (FY2026)