D47.01
✓ BillableCutaneous mastocytosis
Neoplasms (C00-D49)
Also Known As
Diffuse cutaneous mastocytosisMaculopapular cutaneous mastocytosisSolitary mastocytomaTelangiectasia macularis eruptiva perstansUrticaria pigmentosa
❌ Excludes1
directCannot be coded with D47.01
- • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
- • congenital urticaria pigmentosa (Q82.2)
- • extracutaneous mastocytoma (D47.09)
❌ Excludes1
inherited from D47.0Rules from parent category D47.0: Mast cell neoplasms of uncertain behavior
- • congenital cutaneous mastocytosis (Q82.2)
- • histiocytic neoplasms of uncertain behavior (D47.Z9)
- • malignant mast cell neoplasm (C96.2-)
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Data Source
CMS ICD-10-CM 2026 Tabular List
Updated October 1, 2025 (FY2026)