D68.1

✓ Billable

Hereditary factor XI deficiency

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)

Check This Code

Also Known As

Hemophilia CPlasma thromboplastin antecedent [PTA] deficiencyRosenthal's disease

❌ Excludes1

inherited

Rules inherited from parent codes in the hierarchy.

D68

• abnormal coagulation profile NOS (R79.1)

⚠️ Excludes2

inherited

Rules inherited from parent codes.

D68

• coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
• coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

Clinical Description

ICD-10-CM code D68.1 represents hereditary factor xi deficiency. This code falls under the Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) classification. It is a billable/specific code valid for HIPAA-covered transactions as of October 1, 2025 (FY2026). This code can be used to indicate a diagnosis for reimbursement purposes on insurance claims.

This is a 5-character code at the 4th level of specificity. This is the most specific code available in this subcategory. Coders should note that D68.1 has 1 Excludes1 restriction(s) — codes that cannot be reported together on the same claim.

Frequently Asked Questions

What is ICD-10 code D68.1?

ICD-10-CM code D68.1 is "Hereditary factor XI deficiency". It belongs to the category: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89).

Is D68.1 a billable ICD-10 code?

Yes, D68.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What codes are excluded with D68.1?

D68.1 has 1 Excludes1 rule(s). These codes are mutually exclusive and cannot be coded together on the same claim.

Can D68.1 be coded with other codes?

D68.1 has 2 Excludes2 note(s). These conditions can be coded together if both are documented in the patient record.

Related Codes in D68

Other codes in the same category that may be relevant for differential coding:

D68.0Von Willebrand disease D68.2Hereditary deficiency of other clotting factors D68.3Hemorrhagic disorder due to circulating anticoagulants D68.4Acquired coagulation factor deficiency D68.5Primary thrombophilia D68.6Other thrombophilia D68.8Other specified coagulation defects D68.9Coagulation defect, unspecified

🧪 Validate Combinations

Add D68.1 to the Excludes Checker to validate against your full code list.

Open in Checker →

Code Information

CodeD68.1

BillableYes

ParentD68

CategoryDiseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)

Excludes11 rule(s)

Excludes22 note(s)

Data Source

CMS ICD-10-CM 2026 Tabular List

Updated October 1, 2025 (FY2026)