D84.1

✓ Billable

Defects in the complement system

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)

Also Known As

C1 esterase inhibitor [C1-INH] deficiency

✅ No additional coding notes for D84.1

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Code Information

CodeD84.1

BillableYes

ParentD84

CategoryDiseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)

Excludes10 rule(s)

Excludes20 note(s)

Data Source

CMS ICD-10-CM 2026 Tabular List

Updated October 1, 2025 (FY2026)