E78.00

Billable

Pure hypercholesterolemia, unspecified

Endocrine, nutritional and metabolic diseases (E00-E89)

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Also Known As

Fredrickson's hyperlipoproteinemia, type IIaHyperbetalipoproteinemiaLow-density-lipoprotein-type [LDL] hyperlipoproteinemia(Pure) hypercholesterolemia NOS
No additional coding notes for E78.00

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Code Information

CodeE78.00
BillableYes
ParentE78.0
CategoryEndocrine, nutritional and metabolic diseases (E00-E89)
Excludes10 rule(s)
Excludes20 note(s)

Data Source

CMS ICD-10-CM 2026 Tabular List

Updated October 1, 2025 (FY2026)