E78.3

Billable

Hyperchylomicronemia

Endocrine, nutritional and metabolic diseases (E00-E89)

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Also Known As

Chylomicron retention diseaseFredrickson's hyperlipoproteinemia, type I or VHyperlipidemia, group DMixed hyperglyceridemia

Excludes1

inherited from E78

Rules from parent category E78: Disorders of lipoprotein metabolism and other lipidemias

  • sphingolipidosis (E75.0-E75.3)

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Code Information

CodeE78.3
BillableYes
ParentE78
CategoryEndocrine, nutritional and metabolic diseases (E00-E89)
Excludes11 rule(s)
Excludes20 note(s)

Data Source

CMS ICD-10-CM 2026 Tabular List

Updated October 1, 2025 (FY2026)