E78.6
✓ BillableLipoprotein deficiency
Endocrine, nutritional and metabolic diseases (E00-E89)
Also Known As
AbetalipoproteinemiaDepressed HDL cholesterolHigh-density lipoprotein deficiencyHypoalphalipoproteinemiaHypobetalipoproteinemia (familial)Lecithin cholesterol acyltransferase deficiencyTangier disease
❌ Excludes1
inherited from E78Rules from parent category E78: Disorders of lipoprotein metabolism and other lipidemias
- • sphingolipidosis (E75.0-E75.3)
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CodeE78.6
BillableYes
ParentE78
CategoryEndocrine, nutritional and metabolic diseases (E00-E89)
Excludes11 rule(s)
Excludes20 note(s)
Data Source
CMS ICD-10-CM 2026 Tabular List
Updated October 1, 2025 (FY2026)