M04.2

✓ Billable

Cryopyrin-associated periodic syndromes

Diseases of the musculoskeletal system and connective tissue (M00-M99)

Check This Code

Also Known As

Chronic infantile neurological, cutaneous and articular syndrome [CINCA]Familial cold autoinflammatory syndromeFamilial cold urticariaMuckle-Wells syndromeNeonatal onset multisystemic inflammatory disorder [NOMID]

⚠️ Excludes2

inherited

Rules inherited from parent codes.

  • Crohn's disease (K50.-)

Clinical Description

ICD-10-CM code M04.2 represents cryopyrin-associated periodic syndromes. This code falls under the Diseases of the musculoskeletal system and connective tissue (M00-M99) classification. It is a billable/specific code valid for HIPAA-covered transactions as of October 1, 2025 (FY2026). This code can be used to indicate a diagnosis for reimbursement purposes on insurance claims.

This is a 5-character code at the 4th level of specificity. This is the most specific code available in this subcategory.

Frequently Asked Questions

What is ICD-10 code M04.2?

ICD-10-CM code M04.2 is "Cryopyrin-associated periodic syndromes". It belongs to the category: Diseases of the musculoskeletal system and connective tissue (M00-M99).

Is M04.2 a billable ICD-10 code?

Yes, M04.2 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

Can M04.2 be coded with other codes?

M04.2 has 1 Excludes2 note(s). These conditions can be coded together if both are documented in the patient record.

Related Codes in M04

Other codes in the same category that may be relevant for differential coding:

🧪 Validate Combinations

Add M04.2 to the Excludes Checker to validate against your full code list.

Open in Checker →

Code Information

CodeM04.2
BillableYes
ParentM04
CategoryDiseases of the musculoskeletal system and connective tissue (M00-M99)
Excludes10 rule(s)
Excludes21 note(s)

Data Source

CMS ICD-10-CM 2026 Tabular List

Updated October 1, 2025 (FY2026)