Q27.1
✓ BillableCongenital renal artery stenosis
Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
⚠️ Excludes2
inheritedRules inherited from parent codes.
- • anomalies of cerebral and precerebral vessels (Q28.0-Q28.3)
- • anomalies of coronary vessels (Q24.5)
- • anomalies of pulmonary artery (Q25.5-Q25.7)
- • congenital retinal aneurysm (Q14.1)
- • hemangioma and lymphangioma (D18.-)
Clinical Description
ICD-10-CM code Q27.1 represents congenital renal artery stenosis. This code falls under the Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0) classification. It is a billable/specific code valid for HIPAA-covered transactions as of October 1, 2025 (FY2026). This code can be used to indicate a diagnosis for reimbursement purposes on insurance claims.
This is a 5-character code at the 4th level of specificity. This is the most specific code available in this subcategory.
Frequently Asked Questions
What is ICD-10 code Q27.1?
ICD-10-CM code Q27.1 is "Congenital renal artery stenosis". It belongs to the category: Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0).
Is Q27.1 a billable ICD-10 code?
Yes, Q27.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
Can Q27.1 be coded with other codes?
Q27.1 has 5 Excludes2 note(s). These conditions can be coded together if both are documented in the patient record.
Related Codes in Q27
Other codes in the same category that may be relevant for differential coding:
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Data Source
CMS ICD-10-CM 2026 Tabular List
Updated October 1, 2025 (FY2026)