Q85.83

✓ Billable

Von Hippel-Lindau syndrome

Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

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❌ Excludes1

inherited

Rules inherited from parent codes in the hierarchy.

  • Meckel-Gruber syndrome (Q61.9)
  • ataxia telangiectasia [Louis-Bar] (G11.3)
  • familial dysautonomia [Riley-Day] (G90.1)

Clinical Description

ICD-10-CM code Q85.83 represents von hippel-lindau syndrome. This code falls under the Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0) classification. It is a billable/specific code valid for HIPAA-covered transactions as of October 1, 2025 (FY2026). This code can be used to indicate a diagnosis for reimbursement purposes on insurance claims.

This is a 6-character code at the 5th level of specificity. This is the most specific code available in this subcategory. Coders should note that Q85.83 has 3 Excludes1 restriction(s) — codes that cannot be reported together on the same claim.

Frequently Asked Questions

What is ICD-10 code Q85.83?

ICD-10-CM code Q85.83 is "Von Hippel-Lindau syndrome". It belongs to the category: Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0).

Is Q85.83 a billable ICD-10 code?

Yes, Q85.83 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What codes are excluded with Q85.83?

Q85.83 has 3 Excludes1 rule(s). These codes are mutually exclusive and cannot be coded together on the same claim.

Related Codes in Q85.8

Other codes in the same category that may be relevant for differential coding:

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Code Information

CodeQ85.83
BillableYes
ParentQ85.8
CategoryCongenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
Excludes13 rule(s)
Excludes20 note(s)

Data Source

CMS ICD-10-CM 2026 Tabular List

Updated October 1, 2025 (FY2026)