Q87.4

⚠ Non-billable (Header)

Marfan syndrome

Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

⚠️ This is a category header code — not billable. Use a more specific child code below.

Check This Code

📋 Code Instructions

inherited

Q87

• code(s) to identify all associated manifestations

Child Codes (4)

Q87.40Marfan syndrome, unspecified✓ Billable Q87.41Marfan syndrome with cardiovascular manifestationsHeader Q87.42Marfan syndrome with ocular manifestations✓ Billable Q87.43Marfan syndrome with skeletal manifestation✓ Billable

Clinical Description

ICD-10-CM code Q87.4 represents marfan syndrome. This code falls under the Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0) classification. It is a non-billable category header code. A more specific child code from the list below must be used for billing and reimbursement purposes.

This is a 5-character code at the 4th level of specificity. There are 4 more specific child codes under Q87.4.

Frequently Asked Questions

What is ICD-10 code Q87.4?

ICD-10-CM code Q87.4 is "Marfan syndrome". It belongs to the category: Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0).

Is Q87.4 a billable ICD-10 code?

No, Q87.4 is a non-billable header code. A more specific child code must be used for billing.

Related Codes in Q87

Other codes in the same category that may be relevant for differential coding:

Q87.0Congenital malformation syndromes predominantly affecting facial appearance Q87.1Congenital malformation syndromes predominantly associated with short stature Q87.2Congenital malformation syndromes predominantly involving limbs Q87.3Congenital malformation syndromes involving early overgrowth Q87.5Other congenital malformation syndromes with other skeletal changes Q87.8Other specified congenital malformation syndromes, not elsewhere classified

🧪 Validate Combinations

Add Q87.4 to the Excludes Checker to validate against your full code list.

Open in Checker →

Code Information

CodeQ87.4

BillableNo — Header code

ParentQ87

CategoryCongenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

Excludes10 rule(s)

Excludes20 note(s)

Child codes4

Data Source

CMS ICD-10-CM 2026 Tabular List

Updated October 1, 2025 (FY2026)