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D81.39

✓ Billable

Other adenosine deaminase deficiency

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)

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Also Known As

Adenosine deaminase [ADA] deficiency type 1, NOSAdenosine deaminase [ADA] deficiency type 1, without SCIDAdenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiencyPartial ADA deficiency (type 1)Partial adenosine deaminase deficiency (type 1)

❌ Excludes1

inherited

Rules inherited from parent codes in the hierarchy.

D81
  • • autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

Clinical Description

ICD-10-CM code D81.39 represents other adenosine deaminase deficiency. This code falls under the Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) classification. It is a billable/specific code valid for HIPAA-covered transactions as of October 1, 2025 (FY2026). This code can be used to indicate a diagnosis for reimbursement purposes on insurance claims.

This is a 6-character code at the 5th level of specificity. This is the most specific code available in this subcategory. Coders should note that D81.39 has 1 Excludes1 restriction(s) — codes that cannot be reported together on the same claim.

Frequently Asked Questions

What is ICD-10 code D81.39?

ICD-10-CM code D81.39 is "Other adenosine deaminase deficiency". It belongs to the category: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89).

Is D81.39 a billable ICD-10 code?

Yes, D81.39 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What codes are excluded with D81.39?

D81.39 has 1 Excludes1 rule(s). These codes are mutually exclusive and cannot be coded together on the same claim.

Related Codes in D81.3

Other codes in the same category that may be relevant for differential coding:

D81.30Adenosine deaminase deficiency, unspecifiedD81.31Severe combined immunodeficiency due to adenosine deaminase deficiencyD81.32Adenosine deaminase 2 deficiency

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Code Information

CodeD81.39
BillableYes
ParentD81.3
CategoryDiseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Excludes11 rule(s)
Excludes20 note(s)

Data Source

CMS ICD-10-CM 2026 Tabular List

Updated October 1, 2025 (FY2026)