D81.818
✓ BillableOther biotin-dependent carboxylase deficiency
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Also Known As
Holocarboxylase synthetase deficiencyOther multiple carboxylase deficiency
❌ Excludes1
inherited from D81.81Rules from parent category D81.81: Biotin-dependent carboxylase deficiency
- • biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)
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CodeD81.818
BillableYes
ParentD81.81
CategoryDiseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Excludes11 rule(s)
Excludes20 note(s)
Data Source
CMS ICD-10-CM 2026 Tabular List
Updated October 1, 2025 (FY2026)