ICD10Check
CheckerBrowseOpen

D81.819

✓ Billable

Biotin-dependent carboxylase deficiency, unspecified

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)

Check This Code

Also Known As

Multiple carboxylase deficiency, unspecified

❌ Excludes1

inherited from D81.81

Rules from parent category D81.81: Biotin-dependent carboxylase deficiency

  • • biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)

🧪 Validate Combinations

Add D81.819 to the Excludes Checker to validate against your full code list.

Open in Checker →

Code Information

CodeD81.819
BillableYes
ParentD81.81
CategoryDiseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Excludes11 rule(s)
Excludes20 note(s)

Data Source

CMS ICD-10-CM 2026 Tabular List

Updated October 1, 2025 (FY2026)